Long QT Syndrome (LQTS)

Long QT Syndrome (LQTS)

This PedsCases note provides a one-page overview on Long QT Syndrome, inlcuding its etiology, pathophysiology, diagnosis and management. It was created by Lize-Mari du Toit, a medical student at the University of Alberta with the help of Dr. Michal Kantoch, a pediatric cardiologist at the University of Alberta. 

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Video: Approach to Pediatric ECG

 

References

  1. Park, M. K., & Guntheroth, W. G. (2006). How to read pediatric ECGs (Vol. 847). Elsevier Health Sciences.

  2. Acquired long QT syndrome: Definitions, pathophysiology, and causes. (n.d.). In UpToDate. Retrieved August 1, 2024, from https://www.uptodate.com/contents/acquired-long-qt-syndrome-definitions-pathophysiology-and-causes

  3. Acquired long QT syndrome: Clinical manifestations, diagnosis, and management. (n.d.). In UpToDate. Retrieved August 1, 2024, from https://www.uptodate.com/contents/acquired-long-qt-syndrome-clinical-manifestations-diagnosis-and-management

  4. Congenital long QT syndrome: Pathophysiology and genetics. (n.d.). In UpToDate. Retrieved August 1, 2024, from https://www.uptodate.com/contents/congenital-long-qt-syndrome-pathophysiology-and-genetics

  5. Congenital long QT syndrome: Diagnosis. (n.d.). In UpToDate. Retrieved August 1, 2024, from https://www.uptodate.com/contents/congenital-long-qt-syndrome-diagnosis

  6. Congenital long QT syndrome: Epidemiology and clinical manifestations. (n.d.). In UpToDate. Retrieved August 1, 2024, from https://www.uptodate.com/contents/congenital-long-qt-syndrome-epidemiology-and-clinical-manifestations

  7. Sudden Arrhythmia Death Syndromes (SADS) Foundation. (n.d.). Long QT syndrome. Retrieved August 1, 2024, from https://sads.org/sads-conditions/long-qt-syndrome/

  8. Schwartz, P. J., Crotti, L., & Insolia, R. (2012). Long-QT syndrome: from genetics to management. Circulation: Arrhythmia and Electrophysiology, 5(4), 868-877.

  9. Nandita Sharma, Daniel Cortez, Kristin Disori, Jason R. Imundo, Michael Beck; A Review of Long QT Syndrome: Everything a Hospitalist Should Know. Hosp Pediatr April 2020; 10 (4): 369–375. https://doi.org/10.1542/hpeds.2019-0139

 

Physiologic System: